Abst1100 #ACR2021 @RheumNow PAH in AOSD rare, mostly in polycyclic disease, associated w/flares (85%). overall survival 93% at 1 year and 74% at 3 years. PAH was severe at diagnosis: 2 (15%), 7 (54%) and 4 (31%) patients were in NYHA functional class II, III and IV, respectively. https://t.co/x20LooA2G7