Hemophagocytic Syndrome in Adults Save

Hemophagocytic lymphohistiocytosis(HLH) is a rare complication of many disorders. In children, systemic JIA is by far the most common cause of HLH. In this review of 73 adult patients from an academic center the most common associations were with infections (41.1%), malignancies (28.8%), autoimmune disorders (6.8%) and idiopathic disorders (17.8%).